View of the clinic, diagnosis and treatment of familial benign pemphigus (Hailey — Hailey disease). Literature review

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Abstract


The article describes modern views on predisposing factors, histological and genetic changes, the role of ATP2C1 encoding a mutant gene, localized on chromosome 3 in the pathogenesis of Hailey — Hailey disease. Diagnostic criteria, differential diagnostics with other diseases and methods of modern treatment of this disease are presented.


About the authors

M. V. Drozhdina

Kirov State Medical University

Author for correspondence.
Email: drozhdina@yandex.ru

Russian Federation

Cand. Sci. (Med.), Assoc. Prof., Department of Dermatovenerology and Cosmetology

K Marks str., 112, Kirov, 610027, Russian Federation

S. V. Koshkin

Kirov State Medical University

Email: koshkin_sergei@mail.ru

Russian Federation

Dr. Sci. (Med.), Prof., Departmental Head, Department of Dermatovenereology and Cosmetology

K Marks str., 112, Kirov, 610027, Russian Federation

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