View of the clinic, diagnosis and treatment of familial benign pemphigus (Hailey — Hailey disease). Literature review

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Abstract


The article describes modern views on predisposing factors, histological and genetic changes, the role of ATP2C1 encoding a mutant gene, localized on chromosome 3 in the pathogenesis of Hailey — Hailey disease. Diagnostic criteria, differential diagnostics with other diseases and methods of modern treatment of this disease are presented.


M. V. Drozhdina

Kirov State Medical University

Author for correspondence.
Email: drozhdina@yandex.ru

Russian Federation

Cand. Sci. (Med.), Assoc. Prof., Department of Dermatovenerology and Cosmetology

K Marks str., 112, Kirov, 610027, Russian Federation

S. V. Koshkin

Kirov State Medical University

Email: koshkin_sergei@mail.ru

Russian Federation

Dr. Sci. (Med.), Prof., Departmental Head, Department of Dermatovenereology and Cosmetology

K Marks str., 112, Kirov, 610027, Russian Federation

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